Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease

Front Cover
Vincent Cottin, Jean-Francois Cordier, Luca Richeldi
Springer, Jan 10, 2015 - Medical - 625 pages
Orphan Lung Diseases: A Clinical Guide to Rare Lung Disease provides a comprehensive, clinically focused textbook on rare and so-called ‘orphan’ pulmonary diseases. The book is oriented towards the diagnostic approach, including manifestations suggesting the disease, diagnostic criteria, methods of diagnostic confirmation, and differential diagnosis, with an overview of management.
 

Contents

Orphan Lung Diseases from Definition to Organisation of Care
2
The Challenges of Clinical Research in Orphan Diseases
5
Chronic Bronchiolitis in Adults
16
Diffuse Bronchiectasis of Genetic Origin
29
Allergic Bronchopulmonary Mycosis
52
Orphan Tracheopathies
73
Amyloidosis and the Respiratory Tract
90
Eosinophilic Granulomatosis with Polyangiitis ChurgStrauss Syndrome A Clinical and Therapeutic Approach ...
113
Pulmonary Alveolar Microlithiasis
305
Pulmonary Fibrosis and the Many Faces of UIP
314
The Syndrome of Combined Pulmonary Fibrosis and Emphysema
327
Nonspecific Unclassifiable and Rare Idiopathic Interstitial Pneumonia Acute Interstitial Pneumonia Respiratory Bronchiolitis Interstitial Pneumonia D...
348
Organizing Pneumonias
363
Interstitial Lung Disease in Systemic Sclerosis
379
Interstitial Lung Disease in Connective Tissue Diseases Other Than Systemic Sclerosis
391
Interstitial Lung Disease in Undifferentiated Forms of Connective Tissue Disease
419

Granulomatosis with Polyangiitis Wegeners Granulomatosis
126
Alveolar Hemorrhage
155
Pulmonary Involvement in Takayasu Arteritis and Behçet Disease
176
Pulmonary Vascular Manifestations of Hereditary Hemorrhagic Telangiectasia
191
Hepatopulmonary Syndrome
201
Nonlangerhans Cell HistiocytosisIncluding ErdheimChester Disease and the Lung
211
Eosinophilic Pneumonia
227
Multiple Cystic Lung Diseases
253
Lymphangioleiomyomatosis
271
Pulmonary Alveolar Proteinosis
284
Exogenous Lipoid Pneumonia
295
Pulmonary Langerhans Cell Histiocytosis and SmokingRelated Interstitial Lung Diseases
435
Rare Causes and the Spectrum of Hypersensitivity Pneumonitis
457
Chronic Beryllium Disease and Other Interstitial Lung Diseases of Occupational Origin
473
Lymphoproliferative Lung Disorders
493
Pulmonary Manifestations of Hematological Malignancies Focus on Pulmonary Chronic GraftVersus Host Disease ...
516
Pulmonary Hypertension in Orphan Lung Diseases
529
Rare and Emergent DrugInduced and Iatrogenic Respiratory Conditions A Guide to Their Recognition and Management ...
540
From Cancer Mimicking Orphan Lung Disease to Orphan Thoracic Oncology
581
Rare Diffuse Lung Diseases of Genetic Origin
597
Index
611
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